피크노디소스토시스 환자의 악안면기형에 대한 단계적 치료
Staged Approach to Correct Dentofacial Deformity of Pycnodysostosis
김용덕, 손우성, 최나래,
소속 상세정보
김용덕 ( Kim Yong-Deok ) - 부산대학교 치의학전문대학원 구강악안면외과학교실
손우성 ( Son Woo-Sung ) - 부산대학교 치의학전문대학원 치과교정학교실
최나래 ( Choi Na-Rae ) - 부산대학교 치의학전문대학원 구강악안면외과학교실
Abstract
Pycnodysostosis (PDO) is a human autosomal recessive genetic disorder characterized by osteosclerosis of the skeleton, short statue, and severe bone fragility. This unusual syndrome usually involved typical craniomaxillofacial deformities which were composed with hypoplastic midface, collapsed palate, open mouth posture, beaked nose, micrognathia, anterior crossbite, dental crowding and over-retained deciduous teeth. Early diagnosis and intervention are mandatory. The present study reported staged approach case for a PDO patient to correct his dentofacial deformity.
키워드
Dwarfism; Distraction osteogenesis; Orthognathic surgery; Complication; Quality of life
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